Thoracic Insufficiency Syndrome

Thoracic Insufficiency Syndrome
Other Diseases

There are other diseases that can affect thoracic volume without necessarily causing spine deformity. Jeune syndrome, in which there is a severe narrowing of the chest due to the failure of the ribs to grow, is an example of this phenomenon. This causes a hypoplastic (small) thorax, constricting the lungs from each side because of the narrow rib cage. Hypoplastic thorax can also be caused by a compromise in the height of the thorax in conditions such as Jarcho-Levine syndrome. Both of these syndromes are rare, but have a high mortality rate from respiratory problems early in life.

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The Scoliosis Research Society provides information on these web pages regarding research and links as a public service. The SRS believes that patients should contact their treating physician about the relevance of any information listed on the site prior to proceeding with any particular treatment. Just as no two individuals are exactly alike, no two patients with a spinal deformity are the same. Therefore, your spinal deformity surgeon will be the most important source of information about the management of your particular spinal problem.